2025 ICD-10-CM Diagnosis Code E00.9

Congenital iodine-deficiency syndrome, unspecified

• E00.9 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
• The 2025 edition of ICD-10-CM E00.9 became effective on October 1, 2024.
• This is the American ICD-10-CM version of E00.9 – other international versions of ICD-10 E00.9 may differ.

Applicable To

• Congenital iodine-deficiency hypothyroidism NOS
• Endemic cretinism NOS

The following code(s) above E00.9 contain annotation back-references

 that may be applicable to E00.9:

• E00-E89  Endocrine, nutritional and metabolic diseases
• E00  Congenital iodine-deficiency syndrome

Approximate Synonyms

• Congenital iodine deficiency syndrome
• Endemic cretinism

Clinical Information

• Severely reduced physical and mental growth associated with pyramidal and extrapyramidal signs and symptoms, due to dietary iodine deficiency.

ICD-10-CM E00.9 is grouped within Diagnostic Related Group(s) (MS-DRG v42.0):

• 643 Endocrine disorders with mcc
• 644 Endocrine disorders with cc
• 645 Endocrine disorders without cc/mcc

Convert E00.9 to ICD-9-CMCode History

• 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
• 2017 (effective 10/1/2016): No change
• 2018 (effective 10/1/2017): No change
• 2019 (effective 10/1/2018): No change
• 2020 (effective 10/1/2019): No change
• 2021 (effective 10/1/2020): No change
• 2022 (effective 10/1/2021): No change
• 2023 (effective 10/1/2022): No change
• 2024 (effective 10/1/2023): No change
• 2025 (effective 10/1/2024): No change

Diagnosis Index entries containing back-references to E00.9:

• Cretin, cretinism (congenital) (endemic) (nongoitrous) (sporadic) E00.9
• MyopathyG72.9
  • in (due to)
    • cretinism E00.9
• Syndrome – see also Disease
  • iodine-deficiency, congenital E00.9