Classical phenylketonuria
- E70.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
- The 2025 edition of ICD-10-CM E70.0 became effective on October 1, 2024.
- This is the American ICD-10-CM version of E70.0 – other international versions of ICD-10 E70.0 may differ.
The following code(s) above E70.0 contain annotation back-references
that may be applicable to E70.0:
Approximate Synonyms
- Dihydropteridine reductase deficiency
- Phenylketonuria
- Phenylketonuria, classical
Clinical Information
- A genetic disorder in which the body lacks the enzyme necessary to metabolize protein
ICD-10-CM E70.0 is grouped within Diagnostic Related Group(s) (MS-DRG v42.0):
- 642 Inborn and other disorders of metabolism
Convert E70.0 to ICD-9-CMCode History
- 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
- 2017 (effective 10/1/2016): No change
- 2018 (effective 10/1/2017): No change
- 2019 (effective 10/1/2018): No change
- 2020 (effective 10/1/2019): No change
- 2021 (effective 10/1/2020): No change
- 2022 (effective 10/1/2021): No change
- 2023 (effective 10/1/2022): No change
- 2024 (effective 10/1/2023): No change
- 2025 (effective 10/1/2024): No change
Diagnosis Index entries containing back-references to E70.0:
- Disorder (of) – see also Disease
- metabolism NOSE88.9
- amino-acidE72.9
- aromaticE70.9
- hyperphenylalaninemiaE70.1
- classical phenylketonuria E70.0
- hyperphenylalaninemiaE70.1
- aromaticE70.9
- amino-acidE72.9
- metabolism NOSE88.9
- Følling’s disease E70.0
- Oligophrenia – see also Disability, intellectual
- phenylpyruvic E70.0
- PhenylketonuriaE70.1
- classical E70.0