2025 ICD-10-CM Diagnosis Code E74.0

Glycogen storage disease

E74.0 should not be used for reimbursement purposes as there are multiple codes below it that contain a greater level of detail.
The 2025 edition of ICD-10-CM E74.0 became effective on October 1, 2024.
This is the American ICD-10-CM version of E74.0 – other international versions of ICD-10 E74.0 may differ.

The following code(s) above E74.0 contain annotation back-references

that may be applicable to E74.0:

Clinical Information

A group of inherited metabolic disorders involving the enzymes responsible for the synthesis and degradation of glycogen. In some patients, prominent liver involvement is presented. In others, more generalized storage of glycogen occurs, sometimes with prominent cardiac involvement.
An inherited metabolic disorder characterized either by defects in glycogen synthesis or defects in the breaking down of glycogen. It results either in the creation of abnormal forms of glycogen or accumulation of glycogen in the tissues.
Any of a group of metabolic disorders characterized by excessive storage of glycogen.

Code History

2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
2017 (effective 10/1/2016): No change
2018 (effective 10/1/2017): No change
2019 (effective 10/1/2018): No change
2020 (effective 10/1/2019): No change
2021 (effective 10/1/2020): No change
2022 (effective 10/1/2021): No change
2023 (effective 10/1/2022): No change
2024 (effective 10/1/2023): No change
2025 (effective 10/1/2024): No change

Code annotations containing back-references to E74.0: