2025 ICD-10-CM Diagnosis Code K00.5

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Hereditary disturbances in tooth structure, not elsewhere classified

  • K00.5 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
  • Short description: Hereditary disturbances in tooth structure, NEC
  • The 2025 edition of ICD-10-CM K00.5 became effective on October 1, 2024.
  • This is the American ICD-10-CM version of K00.5 – other international versions of ICD-10 K00.5 may differ.

Applicable To

  • Amelogenesis imperfecta
  • Dentinogenesis imperfecta
  • Odontogenesis imperfecta
  • Dentinal dysplasia
  • Shell teeth

The following code(s) above K00.5 contain annotation back-references

 that may be applicable to K00.5:

  • K00-K95  Diseases of the digestive system
  • K00  Disorders of tooth development and eruption

Approximate Synonyms

  • Hereditary disturbances in tooth structure

Clinical Information

  • A clinically and genetically heterogeneous group of hereditary conditions characterized by malformed dental enamel, usually involving dental enamel hypoplasia and/or tooth hypomineralization.
  • A congenital tooth development disorder caused by mutations in the dspp gene. The teeth are weak, discolored, and translucent.
  • An apparently hereditary disorder of dentin formation, marked by a normal appearance of coronal dentin associated with pulpal obliteration, faulty root formation, and a tendency for peripheral lesions without obvious cause. (from Dorland, 27th ed)
  • An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.

ICD-10-CM K00.5 is grouped within Diagnostic Related Group(s) (MS-DRG v42.0):

  • 011 Tracheostomy for face, mouth and neck diagnoses or laryngectomy with mcc
  • 012 Tracheostomy for face, mouth and neck diagnoses or laryngectomy with cc
  • 013 Tracheostomy for face, mouth and neck diagnoses or laryngectomy without cc/mcc
  • 157 Dental and oral diseases with mcc
  • 158 Dental and oral diseases with cc
  • 159 Dental and oral diseases without cc/mcc

Convert K00.5 to ICD-9-CMCode History

  • 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
  • 2017 (effective 10/1/2016): No change
  • 2018 (effective 10/1/2017): No change
  • 2019 (effective 10/1/2018): No change
  • 2020 (effective 10/1/2019): No change
  • 2021 (effective 10/1/2020): No change
  • 2022 (effective 10/1/2021): No change
  • 2023 (effective 10/1/2022): No change
  • 2024 (effective 10/1/2023): No change
  • 2025 (effective 10/1/2024): No change

Diagnosis Index entries containing back-references to K00.5:

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