Type 1 Excludes
- personal history of non-Hodgkin lymphoma (Z85.72)
Clinical Information
- A group of malignant lymphomas thought to derive from peripheral t-lymphocytes in lymph nodes and other nonlymphoid sites. They include a broad spectrum of lymphocyte morphology, but in all instances express t-cell markers admixed with epithelioid histiocytes, plasma cells, and eosinophils. Although markedly similar to large-cell immunoblastic lymphoma (lymphoma, large-cell, immunoblastic), this group’s unique features warrant separate treatment.
- Aggressive nodal or extranodal mature (peripheral) t-cell lymphomas that do not belong to the better defined entities of the remainder of mature t-cell lymphomas. This category includes the following variants: lymphoepithelioid cell variant (lennert’s lymphoma), follicular variant, and t-zone variant.
- One of a group of aggressive (fast-growing) non-hodgkin lymphomas that begin in mature t lymphocytes (t cells that have matured in the thymus gland and gone to other lymphatic sites in the body, including lymph nodes, bone marrow, and spleen.)
- One of a group of aggressive (fast-growing) non-hodgkin lymphomas that begins in mature t lymphocytes (t cells that have matured in the thymus gland and goes to other lymphatic sites in the body, including lymph nodes, bone marrow, and spleen.)
- This type of lymphoma is not frequently seen in the western hemisphere. Clinically, with the exception of anaplastic large cell lymphoma, mature t- and nk-cell lymphomas are among the most aggressive of all hematopoietic neoplasms. Representative disease entities include mycosis fungoides, angioimmunoblastic t-cell lymphoma, hepatosplenic t-cell lymphoma, and anaplastic large cell lymphoma.
Codes
- C84 Mature T/NK-cell lymphomas
- C84.0 Mycosis fungoides
- C84.00 …… unspecified site
- C84.01 …… lymph nodes of head, face, and neck
- C84.02 …… intrathoracic lymph nodes
- C84.03 …… intra-abdominal lymph nodes
- C84.04 …… lymph nodes of axilla and upper limb
- C84.05 …… lymph nodes of inguinal region and lower limb
- C84.06 …… intrapelvic lymph nodes
- C84.07 …… spleen
- C84.08 …… lymph nodes of multiple sites
- C84.09 …… extranodal and solid organ sites
- C84.0A …… in remission
- C84.1 Sézary disease
- C84.10 …… unspecified site
- C84.11 …… lymph nodes of head, face, and neck
- C84.12 …… intrathoracic lymph nodes
- C84.13 …… intra-abdominal lymph nodes
- C84.14 …… lymph nodes of axilla and upper limb
- C84.15 …… lymph nodes of inguinal region and lower limb
- C84.16 …… intrapelvic lymph nodes
- C84.17 …… spleen
- C84.18 …… lymph nodes of multiple sites
- C84.19 …… extranodal and solid organ sites
- C84.1A …… in remission
- C84.4 Peripheral T-cell lymphoma, not elsewhere classified
- C84.40 …… unspecified site
- C84.41 …… lymph nodes of head, face, and neck
- C84.42 …… intrathoracic lymph nodes
- C84.43 …… intra-abdominal lymph nodes
- C84.44 …… lymph nodes of axilla and upper limb
- C84.45 …… lymph nodes of inguinal region and lower limb
- C84.46 …… intrapelvic lymph nodes
- C84.47 …… spleen
- C84.48 …… lymph nodes of multiple sites
- C84.49 …… extranodal and solid organ sites
- C84.4A …… in remission
- C84.6 Anaplastic large cell lymphoma, ALK-positive
- C84.60 …… unspecified site
- C84.61 …… lymph nodes of head, face, and neck
- C84.62 …… intrathoracic lymph nodes
- C84.63 …… intra-abdominal lymph nodes
- C84.64 …… lymph nodes of axilla and upper limb
- C84.65 …… lymph nodes of inguinal region and lower limb
- C84.66 …… intrapelvic lymph nodes
- C84.67 …… spleen
- C84.68 …… lymph nodes of multiple sites
- C84.69 …… extranodal and solid organ sites
- C84.6A …… in remission
- C84.7 Anaplastic large cell lymphoma, ALK-negative
- C84.70 …… unspecified site
- C84.71 …… lymph nodes of head, face, and neck
- C84.72 …… intrathoracic lymph nodes
- C84.73 …… intra-abdominal lymph nodes
- C84.74 …… lymph nodes of axilla and upper limb
- C84.75 …… lymph nodes of inguinal region and lower limb
- C84.76 …… intrapelvic lymph nodes
- C84.77 …… spleen
- C84.78 …… lymph nodes of multiple sites
- C84.79 …… extranodal and solid organ sites
- C84.7A …… breast
- C84.7B …… in remission
- C84.A Cutaneous T-cell lymphoma, unspecified
- C84.A0 …… unspecified site
- C84.A1 …… lymph nodes of head, face, and neck
- C84.A2 …… intrathoracic lymph nodes
- C84.A3 …… intra-abdominal lymph nodes
- C84.A4 …… lymph nodes of axilla and upper limb
- C84.A5 …… lymph nodes of inguinal region and lower limb
- C84.A6 …… intrapelvic lymph nodes
- C84.A7 …… spleen
- C84.A8 …… lymph nodes of multiple sites
- C84.A9 …… extranodal and solid organ sites
- C84.AA …… in remission
- C84.Z Other mature T/NK-cell lymphomas
- C84.Z0 …… unspecified site
- C84.Z1 …… lymph nodes of head, face, and neck
- C84.Z2 …… intrathoracic lymph nodes
- C84.Z3 …… intra-abdominal lymph nodes
- C84.Z4 …… lymph nodes of axilla and upper limb
- C84.Z5 …… lymph nodes of inguinal region and lower limb
- C84.Z6 …… intrapelvic lymph nodes
- C84.Z7 …… spleen
- C84.Z8 …… lymph nodes of multiple sites
- C84.Z9 …… extranodal and solid organ sites
- C84.ZA …… in remission
- C84.9 Mature T/NK-cell lymphomas, unspecified
- C84.90 …… unspecified site
- C84.91 …… lymph nodes of head, face, and neck
- C84.92 …… intrathoracic lymph nodes
- C84.93 …… intra-abdominal lymph nodes
- C84.94 …… lymph nodes of axilla and upper limb
- C84.95 …… lymph nodes of inguinal region and lower limb
- C84.96 …… intrapelvic lymph nodes
- C84.97 …… spleen
- C84.98 …… lymph nodes of multiple sites
- C84.99 …… extranodal and solid organ sites
- C84.9A …… in remission
- C84.0 Mycosis fungoides